Hydrocephalus is a medical condition in which cerebrospinal fluid (CSF) accumulates abnormally within the ventricles of the brain, causing increased pressure. CSF is a clear fluid that provides nutrients and protects the brain and spinal cord from injury. Normally, CSF flows through four ventricles and the subarachnoid space, maintaining a balance between its production and absorption. When this balance is disturbed—either due to overproduction, poor absorption, or obstruction—fluid builds up, leading to hydrocephalus.
There are two main types of hydrocephalus: communicating and noncommunicating (obstructive). Communicating hydrocephalus, also known as nonobstructive hydrocephalus, occurs when CSF absorption is impaired even though there is no blockage in the flow between the ventricles and subarachnoid space. A special form, known as normal pressure hydrocephalus, involves enlarged ventricles but normal CSF pressure. Noncommunicating hydrocephalus, or obstructive hydrocephalus, occurs when CSF flow is blocked within the ventricular system. Common causes include obstructions in the Foramen of Monro, Aqueduct of Sylvius, or the Foramina of Luschka and Magendie, as seen in conditions like Chiari malformation.
According to the ICD-10-CM classification, hydrocephalus falls under category G91 for acquired types and Q03 for congenital cases. Codes under G91 include G91.0 (communicating hydrocephalus), G91.1 (obstructive hydrocephalus), G91.2 (normal pressure hydrocephalus), G91.3 (post-traumatic hydrocephalus), and G91.4 (hydrocephalus associated with other diseases). Congenital hydrocephalus codes include Q03.0 (malformation of Aqueduct of Sylvius), Q03.1 (atresia of Foramina of Magendie and Luschka), Q03.8 (other congenital forms), and Q03.9 (unspecified congenital hydrocephalus). When hydrocephalus coexists with spina bifida, category Q05 is used.